2Orthodontics, Faculty of Dentistry, Mustafa Kemal University, Hatay, Turkey
3Prosthodontics, Faculty of Dentistry, Mustafa Kemal University, Hatay, Turkey
4Periodontology, Faculty of Dentistry, Mustafa Kemal University, Hatay, Turkey
Abstract
The Holt-Oram syndrome (HOS) is a genetic disorder with autosomal dominant inheritance associated with anomalies in upper extremities and heart and affects one out of every 100,000 live births. Maxillofacial development is also affected by these skeletal abnormalities. Although there are many studies about the HOS in the literature, the data about the development of oral and maxillofacial development are very few. In this study, evaluation of a child with the HOS is made in terms of dental and gingival health, oral and maxillofacial formation, and cephalometric analysis measurements are made for the 1st time in the literature and identifi ed findings are discussed in company with the literature.
