Early Childhood Caries is a disease that is diagnosed when a child of or under 71 months of age has got his/her primary teeth with one or more caries, missing tooth surfaces or tooth surfaces with filling. Severe Early Childhood Caries (S-ECC) is the most common disease in children, affecting 60% to 90% of children worldwide. Nutritional status and S-ECC can be caused by some behavioural factors associated with poor dietary habits. Therefore, this study was aimed to determine the nutritional status of children with severe early childhood caries. This study was conducted by using a literature review method with a systematic approach and by collecting articles related to research topics on PubMed, ScienceDirect, and Google Scholar. The referenced papers which were used for the purpose of creating this study were published within the last ten years (between 2011 and 2021). The articles were selected using the Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA). They were screened and assessed for eligibility by JBI critical appraisal tools and The Mixed Methods Appraisal Tool (MMAT). 610 studies were identified through the database search, and 16 were included in this systematic review. The studies which were included in this systematic review vary. Ten of the studies have significant results whilst six of them have non-significant results. The reason for this might be either caries being a multifactorial, varied sample population or the research methods differing in each study.